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infantile amaurotic idiocy


1 definition found

infantile amaurotic idiocy - WordNet (r) 2.1 (2005) :

  infantile amaurotic idiocy
      n 1: a hereditary disorder of lipid metabolism occurring most
           frequently in individuals of Jewish descent in eastern
           Europe; accumulation of lipids in nervous tissue results in
           death in early childhood [syn: Tay-Sachs disease, Tay- Sachs
           , Sachs disease, infantile amaurotic idiocy]